August 24, 2010 — A novel sporadic prion protein disease, variably protease-sensitive prionopathy (VPSPr), with distinct features has been described as the first new prion disease since sporadic ...

Prion diseases, such as Creutzfeldt-Jakob Disease (CJD), are fast-moving, fatal dementia syndromes associated with the formation of aggregates of the prion protein, PrP. How these aggregates form ...

Kuru A virtually extinct form of human prion disease of the Fore linguistic group of Papua New Guinea transmitted via ritualistic endocannibalism. Mainly affected women and young children. Some ...

Prion diseases are a group of different conditions that affect your brain and nervous system. They can cause severe dementia or problems with body control that get worse very quickly. They're rare -- ...

Prion diseases are rare and occur due to proteins in the brain that “misfold.” Another name for prion disease is transmissible spongiform encephalopathies (TSEs). There are many types of prion ...

Prion diseases are rare, fatal neurodegenerative disorders caused by misfolded prion proteins (PrP) in the brain. This can lead to memory loss, behavior changes, and movement problems. Prion diseases ...

The misfolded proteins responsible for a fatal neurological illness in deer have a twist. The first detailed structure of an infectious prion that causes chronic wasting disease, or CWD, reveals ...

Researchers this week say their work should upturn the conventional narrative of how Alzheimer’s disease happens. They argue the progression of Alzheimer’s is driven by a very specific form of two ...

As there a disease that can make a young girl to reach menopause before age? Yes, says Prof Henry Onwubiko. He said prion disease can cause the condition. If a young girl contracts the infectious ...

Sporadic CJD (sCJD) Unknown, but widely believed to be due to a spontaneous misfolding of the normal prion protein. Affects mainly people over the age of 60. Common symptoms include ataxia and ...